What is the life expectancy of a child with HRHS?

Prognosis (Outlook) The post-repair prognosis (survival rate) of a child who has undergone a Fontan procedure increases life longevity between 15 and 30 years.

What is HRHS disease?

What part of the heart is affected by hypoplasia?

In this condition, the left side of the heart — including the aorta, aortic valve, left ventricle and mitral valve — is underdeveloped (hypoplastic). As a result, the body doesn’t receive enough oxygenated blood.

Is tricuspid atresia an HRHS?

HRHS may also change how other parts of the heart develop such as: Tricuspid valve—Controls flow of blood from upper and lower chambers of the heart. Called tricuspid atresia if valve is not present. Pulmonary valve—Controls flow of blood out of the heart to the lung.

What is the survival rate of hypoplastic left heart syndrome?

It is fatal without surgical intervention and responsible for 25% to 40% of all neonatal cardiac mortality. Studies have shown 1-year survival for HLHS ranges from 20% to 60%,3–9 with relatively stable 5-year, 10-year, and 15-year survival of ∼40%.

What are the chances of having a second baby with CHD?

Individuals who have a personal or family history of CHD have a higher chance of a heart defect happening again in the family. For most people, the risk of having another child with a congenital heart defect ranges from 3-5 percent. However, for those who have particularly rare conditions, the risk can go up to 50%.

What is the treatment for hypoplastic left heart syndrome?

Hypoplastic left heart syndrome is treated through several surgical procedures or a heart transplant. Your child’s doctor will discuss treatment options with you. If the diagnosis has been made before the baby is born, doctors usually recommend delivery at a hospital with a cardiac surgery center.

What is the life expectancy of HLHS?

Most infants die within the first two weeks of life, with an average age at death of 4.5 days (31,33,34). Some patients with HLHS, however, can survive beyond sixty days, without any surgical intervention through the development of pulmonary hypertension (8,33).

Who is the oldest person with hypoplastic left heart syndrome?

The oldest living person with HLHS is their 30s. Ultimately, the Cribbs hope and pray that Leigh Ann has a long life ahead of her.

How does hypoplastic right heart syndrome ( HRHS ) work?

Hypoplastic Right Heart Syndrome (HRHS) is a range of right-sided congenital heart defects in which the right-sided structures (tricuspid valve, right ventricle and/or pulmonary valve) are underdeveloped or not formed. When these structures are too small or do not function properly, the right side of the heart cannot send enough blood to the lungs.

Is there a cure for hypoplastic right heart syndrome?

There is no cure for hypoplastic right heart syndrome. A three-stage surgical procedure is commonly used to treat the condition. The surgeries rearrange the blood flow within the heart and allow the left ventricles to do the work for the underdeveloped right side of the heart.

How is the pulmonary artery repaired in hypoplastic right heart?

In a stage 1 Norwood procedure for hypoplastic right heart, the main pulmonary artery is separated from the left and right portions of the pulmonary artery and joined with the upper portion of the aorta. The proximal pulmonary artery is connected to the aortic arch, while the narrowed segment of the pulmonary trunk is repaired.